| CASE REPORT |
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| Year : 2016 | Volume
: 4
| Issue : 2 | Page : 222-224 |
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Pure epithelioid angiomyolipoma of kidney in tuberous sclerosis patient: A case report and review of literature
Azar Naimi1, Maryam Riahinejad2, Fereshteh Mohammadizadeh1, Mehrdad Hosseinpour3
1 Department of Pathology, School of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran
2 Department of Radiology, School of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran
3 Department of Surgery, School of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran
Correspondence Address:
Azar Naimi
Department of Pathology, School of Medicine, Isfahan University of Medical Sciences, Isfahan
Iran
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/2321-4848.196201
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The majority of renal angiomyolipoma (AML) is sporadic, and occasionally it occurs in the background of tuberous sclerosis complex. Epithelioid AML (EAML) is an uncommon variant, with uncertain behavior. We present a case of tuberous sclerosis with right large renal tumor. The tumor revealed epithelioid cells accompanied by thick wall vessels and muscular bundles in all the sections; devoid of lipocytes. Immunohistochemistry confirmed the diagnosis of epithelioid perivascular epithelioid cell tumor. Pure EAML is a rare tumor with potential malignancy. Accurate diagnosis, especially differentiation it from renal cell carcinoma, is very important for proper management of the patient. |
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